 Inflammatory Lyomyosarcoma, LMS, is a rare type of cancer that affects the smooth muscles of the body. It is closely related to another rare cancer called histiocytic rabdomyosarcoma, HRRT, which is characterized by the presence of histiocytes. This case report describes a 17-year-old male who presented with a soft tissue mass on the back of his neck. After further investigation, it was determined that he had inflammatory LMS-HRRT. He underwent surgery and radiation therapy and is currently disease-free after 12 months. This article was authored by Bart Recky, Munita BAL, Baskar Thirvath, and others.