 Interlabyrinthine schwannomas, ILS, are rare benign tumors that arise from the peripheral branches of the cochlear and vestibular nerves within the inner ear. These tumors can cause hearing loss and may require surgery for removal. Surgical removal of these tumors can be combined with simultaneous cochlear implantation to restore hearing. A systematic review of the literature was conducted, as well as two case studies from our center at Ospedale University Degli Studi di Padova. The results showed that cochlear implants were successful in restoring hearing in patients with ILS. This article was authored by Sebastiano Franciella, Marzia Ariano, Francesca Bovalaqua, and others.