 Nephrogenic syndrome of inappropriate antidioresis, NSIAD, is an X-link genetic condition caused by mutations in the AVPR2 gene. It leads to uvelemic hyponatremia despite low levels of arginine vasopressin, AVP, resulting in misdiagnosis as hyporenenemic hypoldosteronism, HH. Two cases are reported here, where the first infant was initially diagnosed with HH based on symptoms and laboratory results, but was later found to have NSIAD after further testing. The second infant was also diagnosed with HH, but was eventually identified as having NSIAD when further testing showed a mutation in the AVPR2 gene. Both infants were successfully treated for their hyponatremia with fluid restriction and avoidance of diuretics. This article was authored by Jamala Mamadova, Cengiz Kara, Ida Shalebi-Bitkin and others.