 Hello everyone, I am Dr. Srikanth. I am a consultant, pediatric gastroenterology, hepatology, nutrition at Manipal Hospital's Bangalore. So, biliriatraceae is a condition in which the ducts which are draining the liver is abnormal, where they progressively vanish and disappear. So, because of that the secretions of the fluid, whichever the liver secretes, the bile is not reaching the duodenum and that gets accumulated in the body leading to jaundice. So, this is one of the reasons for pathological jaundice or jaundice because of the severe liver disease in early infancy. So, what are the symptoms? Your child may present with high-colored urine and pale or clay-colored stools and distension of the abdomen or the belly of the infant. So, if the child comes to the hospital in an early stage, we can manage with certain medications and can be treated with minimal surgery what we call as Kasai Porta Entrostomy. If it is in the advanced stage, then we may require a liver transplantation to cure the baby. So, by and large this is one of the most common indication for liver transplantation in early infancy.