 Soft syndrome is a rare genetic disorder characterized by prenatal onset growth retardation, brachydactyly, onicodysplasia, post-pubertyl onset hypotricosis, normal psychomotor development, and facial dysnorphism including dolicosephaly, elongated triangular face, prominent forehead and nose, and abnormal ear structure. The syndrome has been reported in 31 cases worldwide, and this case report presents the audiological and temporal bone radiological findings in a four-year and five-month-old patient with soft syndrome. The patient's bilateral internal acoustic canals were found to be dilated with lobulated contours, which is consistent with the characteristic audiological and temporal bone radiological findings associated with soft syndrome. Regular and detailed audiological and temporal bone radiology evaluations should be conducted in patients with soft syndrome to better understand its characteristics. This article was authored by SemaSatisai, Arson Cartel, Illyftalora Topquoglu and others. We are article.tv, links in the description below.