 Huntington disease, HD, is a rare neurodegenerative disorder characterized by koreatic movements, behavioral and psychiatric disturbances, and dementia. It affects one in 10,000 to 20,000 people in the Caucasian population and typically starts between the ages of 30 to 50. Juvenile HD, JHD, can start before age 20 with behavior disturbances and learning difficulties. The disease is caused by an elongated CAG repeat on chromosome 4 P16.3 in the Huntington gene, and the longer the repeat, the earlier the onset of disease. Diagnosis is based on clinical symptoms and confirmed by DNA determination. There is no cure for HD, but management should be multidisciplinary and focused on improving quality of life. Treatment options include dopamine receptor blocking or depleting agents, medication for depression and aggressive behavior, and full-time care as the disease progresses. The most common cause of death in HD patients is pneumonia, followed by suicide.