spongiform cardiomyopathy by Dr Sajid Dhakam, Dr Nasir Rah

Isolated left ventricular non-compaction



One of major applications of echocardiography is to identify left ventricular systolic function and different forms of cardiomyopathies.

A 37 years old man came with history of progressive shortness of breath for few months and features of congestive cardiac failure without any preceding history of any viral or bacterial infection. EKG showed features of left atrial enlargement and left ventricular hypertrophy. His transthorasic echo showed apical and distal lateral wall hypertrophy with excessive trabeculatoins and intratrabecular recesses. The endocardial structure was two layered with increased noncomacted to compacted ratio. Also noted was severely reduced left ventricular systolic function with ejection fraction of 15%.

Isolated ventricular noncompaction is a rare form of unclassified cardiomyopathy, previously known as "spongy left ventricular myocardium". It has been described in fewer than 100 infants and children while reports in adults are much rarer.

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Science & Technology

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• echocardiography